遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体
- 产地:上海
- 供应商:上海仁捷生物科技有限公司
- 供应商报价: 电议
- 标签:遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体,遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体价格,遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体厂家
产品信息
抗体(antibody)指机体的免疫系统在抗原刺激下,由B淋巴细胞或记忆细胞增殖分化成的浆细胞所产生的、可与相应抗原发生特异性结合的免疫球蛋白。主要分布在血清中,也分布于组织液及外分泌液中。
遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体 产品信息:
中文名称:遗传性失明相关蛋白AIPL1抗体
英文名称:Anti-AIPL1
产品编号:byk-12452R
产品规格:0.1ml/0.2ml
产品用途:科研实验
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遗传性失明相关蛋白AIPL1抗体,Anti-AIPL1抗体 介绍:
The inherited blindness associated protein, aryl hydrocarbon receptor interacting protein-like 1 (AIPL1), interacts with the cell cycle regulator protein NUB1. AIPL1 is crucial for protein folding and stabilization, as well as for protein trafficking. It localizes to the nucleus or cytoplasm and is highly expressed in the pineal gland and the retina. In the retina, AIPL1 is expressed in both developing cone and rod photoreceptors, but it is restricted to rod photoreceptors in the adult human retina. Defects in the gene encoding for AIPL1 can cause Leber congenital amaurosis type IV, an early-onset, inherited autosomal recessive disorder that results in childhood blindness.
保存条件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
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