UBE1/E1 Ubiquitin Activating Enzyme泛素激活酶E1抗体
- 型号：BY-6835R
- 产地：其它
- 供应商：上海科敏生物科技有限公司
- 供应商报价：电议
- 标签：UBE1/E1 Ubiquitin Activating Enzyme泛素激活酶E1抗体,生物试剂,生物制剂,供应UBE1/E1 Ubiquitin Activating Enzyme泛素激活酶E1抗体,上海科敏生物科技有限公司
产品信息
本公司经销UBE1/E1 Ubiquitin Activating Enzyme，泛素激活酶E1抗体，克隆类型为polyclonal，宿主来源是Rabbit，UBE1/E1 Ubiquitin Activating Enzyme泛素激活酶E1抗体可应用于WB、elisa、IP、IF、IHC等实验，欢迎垂询订购！
本公司经销UBE1/E1 Ubiquitin Activating Enzyme，泛素激活酶E1抗体，克隆类型为polyclonal，宿主来源是Rabbit，UBE1/E1 Ubiquitin Activating Enzyme泛素激活酶E1抗体可应用于WB、elisa、IP、IF、IHC等实验，欢迎垂询订购！
货号：BY-6835R
英文名称：Anti-UBE1/E1 Ubiquitin Activating Enzyme
中文名称：泛素激活酶E1抗体
其他名称：名A1S9;A1S9 protein;A1S9T ａnd BN75 temperature sensitivity complementing;A1S9T;A1ST;GXP 1;GXP1;MGC4781;Protein A1S9;Uba1;UBA1_HUMAN;UBE 1 ;UBE 1X;UBE1;UBE1X;Ubiquitin activating enzyme E1;Ubiquitin-activating enzyme E1;Ubiquitin-like modifier-activating enzyme 1.
抗体来源：Rabbit
克隆类型：polyclonal
蛋白分子量：predicted molecular weight: 118kDa
纯化方法：affinity purified by Protein A
交叉反应：hu, mo, rat, Rb, dog
产品介绍：Activates ubiquitin by first adenylating its C-terminal glycine residue with ATP, ａnd thereafter linking this residue to the side chain of a cysteine residue in E1, yielding an ubiquitin-E1 thioester ａnd free AMP.Involvement in disease: Defects in UBA1 are the cause of spinal muscular atrophy X-linked type 2 （SMAX2） ; also known as X-linked lethal infantile spinal muscular atrophy, distal X-linked arthrogryposis multiplex congenita or X-linked arthrogryposis type 1 （AMCX1）. Spinal muscular atrophy refers to a group of neuromuscular disorders characterized by degeneration of the anterior horn cells of the spinal cord, leading to symmetrical muscle weakness ａnd atrophy. SMAX2 is a lethal infantile form presenting with hypotonia, areflexia, ａnd multiple congenital contractures.
